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PRSS56 Rabbit pAb (bs-19444R)  
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50ul/1180.00元
100ul/1980.00元
200ul/2800.00元
大包裝/詢價
產(chǎn)品編號 bs-19444R
英文名稱 PRSS56 Rabbit pAb
中文名稱 絲氨酸蛋白酶56抗體
別    名 MCOP6; Protease serine 56; PRS56_HUMAN; Putative serine protease 56; Serine protease 56.  
研究領(lǐng)域 細胞生物  發(fā)育生物學  神經(jīng)生物學  干細胞  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 (predicted: Human)
產(chǎn)品應用 IHC-P=1:100-500,IHC-F=1:100-500,IF=1:100-500,ICC/IF=1:100-500,ELISA=1:5000-10000
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
理論分子量 63 kDa
檢測分子量
細胞定位 細胞漿 
性    狀 Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human PRSS56: 401-500/603 
亞    型 IgG
純化方法 affinity purified by Protein A
緩 沖 液 0.01M TBS (pH7.4) with 1% BSA, 0.02% Proclin300 and 50% Glycerol.
保存條件 Shipped at 4℃. Store at -20℃ for one year. Avoid repeated freeze/thaw cycles.
注意事項 This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
PubMed PubMed
產(chǎn)品介紹 This gene encodes a protein that contains a peptidase S1 domain and possesses trypsin-like serine protease activity. The encoded protein may play a role in eye development, and mutations in this gene are a cause of autosomal recessive posterior microphthalmos. [provided by RefSeq, Dec 2011]

Subcellular Location:
endoplasmic reticulum

Tissue Specificity:
Expressed neural retina, cornea, sclera and optic nerve.

DISEASE:
A developmental ocular disorder characterized by small malformed eyes. Clinical features are extreme hyperopia due to short axial length with essentially normal anterior segment, steep corneal curvatures, shallow anterior chamber, thick lenses, and thickened scleral wall. Palpebral fissures appear narrow because of relatively deep-set eyes, visual acuity is mildly to moderately reduced, and anisometropic or strabismic amblyopia is common. The fundus of the eye shows crowded optical disks, tortuous vessels, and an abnormal foveal avascular zone.

SWISS:
P0CW18

Gene ID:
646960

Database links:

Entrez Gene: 646960 Human

Entrez Gene: 84618 Mouse

Entrez Gene: 363274 Rat

Omim: 613858 Human

SwissProt: P0CW18 Human

SwissProt: F2YMG0 Mouse

Unigene: 570310 Human



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