强伦轩一级A片在线观看,中文字幕乱码人妻二区三区,鲁鲁狠狠狠7777一区二区,西西4444www无码精品
掃碼關(guān)注公眾號           掃碼咨詢技術(shù)支持           掃碼咨詢技術(shù)服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  關(guān)于我們  聯(lián)系我們
西西4444WWW无码精品,日本强伦轩人妻中文字幕,国产一级a一级a免费视频
首頁 > 產(chǎn)品中心 > 標記一抗 > 產(chǎn)品信息
Rabbit Anti-PDSS2/Cy5 Conjugated antibody (bs-10178R-Cy5)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術(shù)支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產(chǎn)品編號 bs-10178R-Cy5
英文名稱 Rabbit Anti-PDSS2/Cy5 Conjugated antibody
中文名稱 Cy5標記的抑癌蛋白DLP1
別    名 ll-trans-decaprenyl-diphosphate synthase subunit 2; bA59I9.3; C6orf210; Candidate tumor suppressor protein; chromosome 6 open reading frame 210; Decaprenyl pyrophosphate synthase subunit 2; decaprenyl pyrophosphate synthetase subunit 2; Decaprenyl-diphosphate synthase subunit 2; DLP1; DLP1_HUMAN; hDLP1; Pdss2; prenyl (decaprenyl) diphosphate synthase, subunit 2; subunit 2 of decaprenyl diphosphate synthase.  
規(guī)格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 腫瘤  免疫學  信號轉(zhuǎn)導  細胞類型標志物  線粒體  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 (predicted: Dog, Pig, Horse, Rabbit, )
產(chǎn)品應用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 44kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from dog PDSS2
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
The protein encoded by this gene is an enzyme that synthesizes the prenyl side-chain of coenzyme Q, or ubiquinone, one of the key elements in the respiratory chain. The gene product catalyzes the formation of all trans-polyprenyl pyrophosphates from isopentyl diphosphate in the assembly of polyisoprenoid side chains, the first step in coenzyme Q biosynthesis. Defects in this gene are a cause of coenzyme Q10 deficiency.

Function:
Supplies decaprenyl diphosphate, the precursor for the side chain of the isoprenoid quinones ubiquinone-10.

Subunit:
Heterotetramer of 2 DPS1/TPRT and 2 DLP1 subunits.

Subcellular Location:
Mitochondrion (Potential).

DISEASE:
Defects in PDSS2 are the cause of coenzyme Q10 deficiency, primary, type 3 (COQ10D3) [MIM:614652]. A fatal encephalomyopathic form of coenzyme Q10 deficiency with nephritic syndrome. Coenzyme Q10 deficiency is an autosomal recessive disorder with variable manifestations consistent with 5 major phenotypes. The phenotypes include an encephalomyopathic form with seizures and ataxia; a multisystem infantile form with encephalopathy, cardiomyopathy and renal failure; a predominantly cerebellar form with ataxia and cerebellar atrophy; Leigh syndrome with growth retardation; and an isolated myopathic form.

Similarity:
Belongs to the FPP/GGPP synthase family.

Database links:

Entrez Gene: 57107 Human

Entrez Gene: 71365 Mouse

Entrez Gene: 365592 Rat

Omim: 610564 Human

SwissProt: Q86YH6 Human

SwissProt: Q33DR3 Mouse

SwissProt: Q5U2R1 Rat

Unigene: 486095 Human

Unigene: 363225 Mouse

Unigene: 20063 Rat



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 nmgps.com 北京博奧森生物技術(shù)有限公司
通過國際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網(wǎng)安備110107000727號
亚洲AV无码成人精品区国产 | 熟女少妇精品一区二区鲁大师 | 欧美激情三级网址在线观看 | 一区二区三区无码高清 | 性夜黄A片爽免费网站 | 中文字幕亚州无码强奸乱伦亚州有码 | 国产人妻一区二区三区欧美毛片 | 日本成人一区二区三区 | 欧一美一交一配一交一交一视频 | 澳门三级片永久性免费看 | 亚洲一区二区三区三州 | 免费看无码一级A片放24小时 | 影音先锋女人aV鲁色资源网站 | 涩涩视频在线观看免费 | 无码人妻精品一区二区二秋霞影院 | 波多野结衣乳巨码无线观看 | 97精品伊人久久久大香线蕉97 | av免费网站在线观看 | 午夜福利三级理论电影 | 午夜高清无码在线观看 | 亚洲熟妇色 二依 | 国产在线观看国偷精品 | 伦色情理伦片A片AAA毛 | 国产成人AV无码一区二区三区 | 四川少妇搡BBB搡BBB爽爽爽小说 | 91精品无码久久久久久久 | 91茄子视频在线观看 | 又大又粗又硬又猛又黄的高朝视频 | 最好看的2018免费观看在线 | 国产精品福利一区二区三区四季 | 精品肉丝脚一区二区三区 | 几人强行糟蹋人妻HD | 午夜成人免费视频网站 | 亚洲精品成a人在线观看 | 人妻精品久久无码区新狼窝 | 国内精品国产成人国产三级 | 麻豆精品视频在线 | 99无码秘 蜜桃人妻一区二区三区 | 国产高清一区二区三区 | 国产高清在线视频 | 粉嫩尤物少妇视频在线播放 |